Intracranial Haemorrhage as a Fatal Complication of Evans Syndrome: A Case Report

  • Olita Shilpakar Department of General Practice and Emergency Medicine, NAMS, Bir Hospital, Kathmandu, Nepal
  • Bibek Rajbhandari Department of General Practice and Emergency Medicine, Nepal Police Hospital, Kathmandu, Nepal
  • Bipin Karki Department of Critical Care Medicine, Om Hospital and Research Centre, Kathmandu, Nepal
  • Umesh Bogati Department of General Practice and Emergency Medicine, NAMS, Bir Hospital, Kathmandu, Nepal
Keywords: autoimmune, evans syndrome, intracranial haemorrhage

Abstract

Evans syndrome is a rare hematologic disorder characterized by the presence of simultaneous or sequential direct Coombs-positive autoimmune hemolytic anemia (AIHA), immune-mediated thrombocytopenia and/or immune neutropenia without any known underlying etiology. Spontaneous intracranial hemorrhage is a rare and life-threatening complication in patients with Evans syndrome and very few cases have been reported to date. We report a case of a thirty-two- year-old female with intracranial haemorrhage with underlying Evans syndrome who presented with the clinical manifestations of headache, vomiting and altered sensorium and succumbed to the fatal complication despite resuscitative measures. This also emphasizes the importance of early recognition of symptoms and immediate presentation to health care facilities for aggressive management of the patient.

Published
2019-12-17